Aortic thrombosis in a patient with a late diagnosis of Behcet's disease

Ana Bittencourt Detanico; Marcelo Luiz Brandão; Ly de Freitas Fernandes; Carolina Parreira Ribeiro Camelo; Juliano Ricardo Santana dos Santos

doi:10.1590/1677-5449.0065

Case Report

Aortic thrombosis in a patient with a late diagnosis of Behcet's disease

Trombose aórtica em paciente com diagnóstico tardio de Doença de Behçet

Ana Bittencourt Detanico; Marcelo Luiz Brandão; Ly de Freitas Fernandes; Carolina Parreira Ribeiro Camelo; Juliano Ricardo Santana dos Santos

http://dx.doi.org/10.1590/1677-5449.0065 J Vasc Bras, vol.14, n2, p.193-196, 2015

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Abstract

Behcet's disease is form of systemic vasculitis of unknown etiology. One surprising feature is that arterial involvement is less common in this disease than venous forms, accounting for 1 to 7% of patients. In 7 to 30% of cases the vascular symptoms precede the clinical diagnosis of Behcet. We describe the case of a patient with Thromboangiitis Obliterans who was treated with lumbar sympathectomy and an aortobiiliac bypass. Around 1 year later he was diagnosed with Behcet's disease after presenting with oral ulcers, genital ulcers and scaling lesions on the hands.

Keywords

Behcet Syndrome, arteritis, peripheral arterial disease

Resumo

A Doença de Behçet é uma vasculite sistêmica de etiologia desconhecida. O inusitado é que o acometimento arterial nesta doença é menos comum que o venoso, correspondendo a 1 a 7% dos pacientes. Já os sintomas vasculares precedem o diagnóstico clínico de Behçet em 7 a 30%. Relatamos o caso de um paciente portador de Tromboangeíte Obliterante que foi submetido a simpatectomia lombar e derivação aorto-bi-ilíaca. Após cerca de um ano, diagnosticou-se Doença de Behçet, devido a quadro clínico de úlceras orais, genitais e lesões descamativas nas mãos.

Palavras-chave

Síndrome de Behçet, arterite, doença arterial periférica

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Sociedade Brasileira de Angiologia e Cirurgia Vascular (SBACV)"> Sociedade Brasileira de Angiologia e Cirurgia Vascular (SBACV)">

Aortic thrombosis in a patient with a late diagnosis of Behcet's disease

Trombose aórtica em paciente com diagnóstico tardio de Doença de Behçet

Ana Bittencourt Detanico; Marcelo Luiz Brandão; Ly de Freitas Fernandes; Carolina Parreira Ribeiro Camelo; Juliano Ricardo Santana dos Santos

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