Jornal Vascular Brasileiro
https://jvascbras.org/article/doi/10.1590/1677-5449.01115
Jornal Vascular Brasileiro
Case Report

Correção endovascular de pseudoaneurisma toracoabdominal em paciente com Doença de Behçet

Endovascular repair of a thoracoabdominal pseudoaneurysm in a patient with Behçet’s disease

Paula Angeleli Bueno de Camargo; Matheus Bertanha; Regina Moura; Marcone Lima Sobreira; Rodrigo Gibin Jaldin; Ricardo de Alvarenga Yoshida; Rafael Elias Farres Pimenta; Winston Bonetti Yoshida

Downloads: 0
Views: 811

Resumo

Resumo A Doença de Behçet é uma doença inflamatória caracterizada por úlceras genitais e orais recorrentes, uveítes e lesões cutâneas. O envolvimento arterial é raro, sendo mais comuns as degenerações aneurismáticas do que as oclusivas. Neste caso clínico, paciente do sexo feminino, em tratamento de doença de Behçet havia 20 anos, iniciou com dor abdominal progressiva por dois meses, com piora súbita importante, foi submetida à tomografia computadorizada, que mostrou pseudoaneurisma toracoabdominal. A paciente foi submetida a tratamento endovascular com sucesso.

Palavras-chave

doença de Behçet, aneurisma aórtico, aneurisma dissecante, procedimentos endovasculares

Abstract

Abstract Behçet’s disease is an inflammatory disease characterized by recurrent oral and genital ulcers, uveitis and skin lesions. Arterial involvement is rare, but when present aneurysmal degeneration is more common than occlusive disease. This report describes the clinical case of a female patient who had been receiving treatment for Behçet’s disease for twenty years before presenting with abdominal pain that progressed for 2 months before suddenly worsening significantly. A CT scan revealed a thoracoabdominal pseudoaneurysm. She was successfully treated with endovascular repair.

Keywords

Behçet’s disease, aortic aneurysm, dissecting aneurysm, endovascular procedures

References

Criteria for diagnosis of Behcet’s disease. Lancet. 1990;335(8697):1078-80.

Liu CW, Ye W, Liu B, Zeng R, Wu W, Dake MD. Endovascular treatment of aortic pseudoaneurysm in Behcet disease. J Vasc Surg. 2009;50(5):1025-30.

Alpagut U, Ugurlucan M, Dayioglu E. Major arterial involvement and review of Behcet’s disease. Ann Vasc Surg. 2007;21(2):232-9.

Yuan S-M. Pulmonary artery aneurysms in Behçet disease. J Vasc Bras. 2014;13(3):217-28.

Azghari A, Belmir H, Bouayad M. Coeliac trunk aneurysm revealing Behçet disease (2 case reports). J Mal Vasc. 2009;34(5):362-5.

Ullery BW, Pochettino A, Wang GJ, Jackson BM, Fairman RM, Woo EY. Celiac artery aneurysm repair in Behcet disease complicated by recurrent thoracoabdominal aortic aneurysms. Vasc Endovascular Surg. 2010;44(2):146-9.

Hafsa C, Kriaa S, Zbidi M. Superior mesenteric artery aneurysm revealing a Behçet disease: a case report. Ann Cardiol Angeiol. 2006;55(5):291-3.

Bouarhroum A, Sedki N, Bouziane Z. Extracranial carotid aneurysm in Behcet disease: report of two new cases. J Vasc Surg. 2006;43(3):627-30.

Kato E, Isobe Y, Mizuno A. A case of Behçet disease with multiple nodular shadows and aneurysm of the brachiocephalic trunk caused by necrotizing vasculitis. Nihon Kokyuki Gakkai Zasshi. 2006;44(2):111-6.

Belczak SQ, Aun R, Valentim L, Sincos IR, Nascimento LD, Puech-Leão P. Tratamento endovascular de aneurismas da aorta em pacientes com doença de Behçet: relato de dois casos. J Vasc Bras. 2010;9(2):89-94.

Kwon TW, Park SJ, Kim HK, Yoon HK, Kim GE, Yu B. Surgical treatment result of abdominal aortic aneurysm in Behcet’s disease. Eur J Vasc Endovasc Surg. 2008;35(2):173-80.

Kalko Y, Basaran M, Aydin U, Kafa U, Basaranoglu G, Yasar T. The surgical treatment of arterial aneurysms in Behcet disease: a report of 16 patients. J Vasc Surg. 2005;42(4):673-7.

Rampoldi V, Righini P, Trimarchi S, Tolva V, Bonandrini L. Single stage repair of symptomatic type IV thoracoabdominal aortic and iliac aneurysm in Behcet’s disease. Case report. J Cardiovasc Surg (Torino). 2001;42(5):691-4.

O’Leary EA, Sabahi I, Ricotta JJ, Walitt B, Akbari CM. Femoral profunda artery aneurysm as an unusual first presentation of Behcet disease. Vasc Endovascular Surg. 2011;45(1):98-102.

D’Alessandro GS, Machietto RF, Silva SM. Popliteal artery aneurysm as a manifestation of decompensated Behçet’s disease. J Vasc Bras. 2006;5:215-9.

Ohira S, Masuda S, Matsushita T. Nine-year experience of recurrent anastomotic pseudoaneurysms after thoracoabdominal aneurysm graft replacement in a patient with behcet disease. Heart Lung Circ. 2014;23(10):e210-3.

Park JH, Chung JW, Joh JH. Aortic and arterial aneurysms in behcet disease: management with stent-grafts--initial experience. Radiology. 2001;220(3):745-50.

Silva Jr OF, Araújo RHS, Freire EAM. Doença de Behçet cursando com trombose de veia cava superior. J Vasc Bras. 2006;5(1):74-7.

Koc Y, Gullu I, Akpek G. Vascular involvement in Behcet’s disease. J Rheumatol. 1992;19(3):402-10.

Park JH, Han MC, Bettmann MA. Arterial manifestations of Behcet disease. AJR Am J Roentgenol. 1984;143(4):821-5.

Matsumoto T, Uekusa T, Fukuda Y. Vasculo-Behcet’s disease: a pathologic study of eight cases. Hum Pathol. 1991;22(1):45-51.

Pereira AH. Ruptura dos vasa vasorum e hematoma intramural da aorta: um paradigma em mudança. J Vasc Bras. 2010;9(2):57-60.

Kim SW, Lee Y, Kim MD. Outcomes of endovascular treatment for aortic pseudoaneurysm in Behcet’s disease. J Vasc Surg. 2014;59(3):608-14.

Kim WH, Choi D, Kim JS, Ko YG, Jang Y, Shim WH. Effectiveness and safety of endovascular aneurysm treatment in patients with vasculo-Behcet disease. J Endovasc Ther. 2009;16(5):631-6.

Walker TG, Kalva SP, Yeddula K. Clinical practice guidelines for endovascular abdominal aortic aneurysm repair: written by the Standards of Practice Committee for the Society of Interventional Radiology and endorsed by the Cardiovascular and Interventional Radiological Society of Europe and the Canadian Interventional Radiology Association. J Vasc Interv Radiol. 2010;21(11):1632-55.

Sociedade Brasileira de Angiologia e Cirurgia Vascular (SBACV)"> Sociedade Brasileira de Angiologia e Cirurgia Vascular (SBACV)">
5ddece690e8825df3d7279a6 jvb Articles

J Vasc Bras

Share this page
Page Sections