Jornal Vascular Brasileiro
https://jvascbras.org/article/doi/10.1590/1677-5449.202200952
Jornal Vascular Brasileiro
Case Report

Endoscopic lumbar sympathectomy as a treatment option for primary erythromelalgia - case report and review

Simpatectomia lombar endoscópica como escolha de tratamento para eritromelalgia primária - relato de caso e revisão

Marcelo de Paula Loureiro; Pietro Maran Novais; João Augusto Nocera Paulin; Daniel Benzecry de Almeida; Arlindo Nascimento de Lemos Junior

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Abstract

Abstract: Erythromelalgia is a rare disease, involving pain, edema, redness, and hyperthermia in the limbs. It is extremely refractory to drugs, has no defined treatment, and causes psychological comorbidities in the patient. We describe a case of erythromelalgia involving a 17-year-old boy who had been suffering from the disease for almost 4 years prior to finding an effective treatment. A bilateral endoscopic lumbar sympathectomy was performed, limited to L2 and L3 resections. Four weeks after the procedure, the patient’s symptoms were significantly mitigated and at 8 months follow-up he remained almost asymptomatic. Endoscopic lumbar sympathectomy was an effective treatment for primary erythromelalgia in this teenager, with exceptional reduction of his symptoms.

Keywords

lumbar sympathectomy, primary erythromelalgia, teenager, surgery, treatment

Resumo

Resumo: Eritromelalgia é uma doença rara caracterizada por dor, edema, eritema e hipertermia nos membros. É extremamente refratária a medicamentos e não tem um tratamento definido, causando comorbidades psicológicas para o paciente. Descrevemos o caso de um menino de 17 anos que possuía eritromelalgia há quase 4 anos antes de ser submetido a um tratamento efetivo. Foi realizada simpatectomia lombar endoscópica bilateral limitada à ressecção dos gânglios L2 e L3. Após 4 semanas do procedimento, o paciente teve diminuição significativa dos seus sintomas e, com 8 meses de seguimento, permanece praticamente assintomático. A simpatectomia lombar endoscópica foi um tratamento eficaz para eritromelalgia primária em um adolescente, com redução excepcional dos seus sintomas.
 

Palavras-chave

simpatectomia lombar, eritromelalgia primária, adolescente, cirurgia, tratamento

References

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Submitted date:
09/22/2022

Accepted date:
11/16/2022

Sociedade Brasileira de Angiologia e Cirurgia Vascular (SBACV)"> Sociedade Brasileira de Angiologia e Cirurgia Vascular (SBACV)">
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