Doença de Behçet cursando com trombose de veia cava superior

Otacílio Figueiredo da Silva Júnior; Ricardo Henrique de Sousa Araújo; Eutília Andrade Medeiros Freire; Ronaldo Rangel Travassos Júnior; Thiago Emanuel Rodrigues Cavalcante; Tarcísio José Pinheiro Lucena; Norberto de Castro Nogueira Neto; Alessandra Vanessa de Albuquerque Melo

doi:10.1590/S1677-54492006000100015

Relato de Caso

Doença de Behçet cursando com trombose de veia cava superior

Behçet's disease presenting with superior vena cava thrombosis

Otacílio Figueiredo da Silva Júnior; Ricardo Henrique de Sousa Araújo; Eutília Andrade Medeiros Freire; Ronaldo Rangel Travassos Júnior; Thiago Emanuel Rodrigues Cavalcante; Tarcísio José Pinheiro Lucena; Norberto de Castro Nogueira Neto; Alessandra Vanessa de Albuquerque Melo

http://dx.doi.org/10.1590/S1677-54492006000100015 J Vasc Bras, vol.5, n1, p.74-77, 2006

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Resumo

A trombose venosa é o principal acometimento do sistema vascular na doença de Behçet, sendo uma complicação freqüente na evolução clínica dessa patologia, e está mais associada ao sexo masculino. Os autores relatam o caso de uma paciente do sexo feminino que apresentou início da doença há 3 anos com úlceras orais, além de úlceras genitais, e que vem cursando com episódios recorrentes de trombose venosa, sendo a primeira uma trombose venosa profunda no membro inferior direito; a segunda, de jugular interna esquerda; e, por último, uma trombose da veia cava superior.

Palavras-chave

Doença de Behçet, trombose venosa, síndrome da veia cava superior

Abstract

Venous thrombosis is the main hazard to the vascular system in Behçet's disease. It is a frequent complication throughout the clinical evolution of this illness, which is more associated with the male gender. The authors report the case of a female patient with disease onset 3 years ago, showing oral and genital ulcers presenting with recurring episodes of venous thrombosis. The first one was a deep venous thrombosis in the right leg; the second was in the left internal jugular vein; and finally a superior vena cava thrombosis.

Keywords

Behçet's disease, venous thrombosis, superior vena cava syndrome

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Sociedade Brasileira de Angiologia e Cirurgia Vascular (SBACV)"> Sociedade Brasileira de Angiologia e Cirurgia Vascular (SBACV)">

Doença de Behçet cursando com trombose de veia cava superior

Behçet's disease presenting with superior vena cava thrombosis

Otacílio Figueiredo da Silva Júnior; Ricardo Henrique de Sousa Araújo; Eutília Andrade Medeiros Freire; Ronaldo Rangel Travassos Júnior; Thiago Emanuel Rodrigues Cavalcante; Tarcísio José Pinheiro Lucena; Norberto de Castro Nogueira Neto; Alessandra Vanessa de Albuquerque Melo

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