Jornal Vascular Brasileiro
https://jvascbras.org/article/doi/10.1590/S1677-54492010000200014
Jornal Vascular Brasileiro
Relato de Caso

Tratamento endovascular de aneurismas da aorta em pacientes com doença de Behçet: relato de dois casos

Endovascular treatment of aortic aneurysms in patients with Behcet's disease: report of two cases

Sergio Quilici Belczak; Ricardo Aun; Luisa Valentim; Igor Rafael Sincos; Luciano Dias Nascimento; Pedro Puech-Leão

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Resumo

A doença de Behçet, uma vasculite sistêmica de causa desconhecida, pode ser causa de doença aneurismática da aorta em alguns portadores dessa patologia. Nós apresentamos nossa experiência com dois casos de aneurismas aórticos em pacientes com doença de Behçet submetidos à terapêutica endovascular, descrevendo seus respectivos seguimentos. A terapêutica atual, a patofisiologia e os critérios diagnósticos vigentes foram revisados. Concluímos que a técnica endovascular é uma excelente opção terapêutica para certos pacientes com doença de Behçet e que esta deve ser acompanhada de tratamento imunossupressivo adequado.

Palavras-chave

Doença de Behçet, aneurisma aórtico, terapia endovascular

Abstract

Behcet's disease, a systemic vasculitis of unknown etiology, may be the cause of aortic aneurysmal diseases in some patients. We report our experience with two Behcet's disease patients who presented with aortic aneurysms and were submitted to endovascular therapy, and describe their respective follow-ups. Current pathophysiology, diagnosis, and treatment approaches were reviewed. Our experience suggests that the endovascular approach, combined with adequate immunosuppressive treatment, is an excellent therapeutic option for some patients with Behcet's disease suffering from aneurysms.

Keywords

Behcet's disease, aortic aneurysm, endovascular treatment

Referências

Sakane T, Takeno M, Suzuki N, Inaba G. Behcet's disease. N Engl J Med.. 1999;341:1284-91.

Park JH, Chung JW, Joh JH. Aortic and arterial aneurysms in Behcet disease: management with stent-grafts - initial experience. Radiology. 2001;220:745-50.

Silva Júnior OF, Araújo RHS, Freire EAM. Doença de Behçet cursando com trombose de veia cava superior. J Vasc Bras.. 2006;5:74-7.

Gouëffic Y, Pistorius M, Heymann MF, Chaillou P, Patra P. Association of aneurysmal and occlusive lesions in Behçet's disease. Ann Vasc Surg. 2005;19:276-9.

Barlas S. Behçet's disease: An insight from a vascular surgeon's point of view. Acta Chir Belg. 1999;99:274-81.

Nitecki SS, Ofer A, Karram T, Schwartz H, Engel A, Hoffman A. Abdominal aortic aneurysm in Behçet's disease: new treatment options for an old and challenging problem. Isr Med Assoc J. 2004;6:152-5.

Behcet H. Üeber rezidivierende Aphtose durch ein vírus verursachte Geschwüre am Mund, am Auge und an den Genitalien. Dermatol Wochenschr. 1937;105:1152-7.

Behçet's disease: guide to diagnosis of Behçet's disease. Jpn J Ophthalmol. 1974;18:291-4.

Park JH, Han MC, Bettmann MA. Arterial Manifestations of Behcet's disease. AJR Am J Roentgenol. 1984;143:821-5.

Koç Y, Güllü I, Akpek G. Vascular involvement in Behçet's disease. J Rheumatol. 1992;19:402-10.

Kwon TW, Park SJ, Kim HK, Yoon HK, Kim GE, Yu B. Surgical treatment result of abdominal aortic aneurysm in Behçet's disease. Eur J Vasc Endovasc Surg. 2008;35:173-80.

Gürler A, Boyvat A, Türsen U. Clinical manifestations of Behçet's disease: an analysis of 2147 patients. Yonsei Med J. 1997;38:423-7.

Okita Y, Ando M, Minatoya K, Kitamura S, Matsuo H. Multiple pseudoaneurysms of the aortic arch, right subclavian artery, and abdominal aorta in a patient with Behçet's disease. J Vasc Surg. 1998;28:723-6.

Matsumoto T, Uekusa T, Fukuda Y. Vasculo-Behcet's disease: a pathologic study of eight cases. Hum Pathol. 1991;22:45-51.

Vasseur MA, Haulon S, Beregi JP, Le Tourneau T, Prat A, Warembourgh H. Endovascular treatment of abdominal aneurysmal aortitis in Behçet's disease. J Vasc Surg. 1998;27:974-6.

D'Alessandro GA, Machietto RF, Silva SM. Aneurisma de artéria poplítea como manifestação da doença de Behçet descompensada. J Vasc Bras. 2006;5:215-9.

Ugurlucan M, Sayin OA, Surmen B. Complication of Behcet's disease: spontaneous aortic pseudoaneurysm. J Card Surg. 2006;21:589-91.

Kingston M, Ratcliffe JR, Altree M, Merendino KA. Aneurysm after arterial puncture in Behçet's disease. Br Med J. 1979;30:1766-7.

Ascione R, Modi P, Triggiani D, Iannelli G, Spampinato N. Detection of postoperative pseudoaneurysms following abdominal aortic aneurysm repair in Behçet's disease by MRA. J Cardiovasc Surg. 2002;43:251-4.

Kasirajan K, Marek JM, Langsfeld M. Behçet's disease: Endovascular management of a ruptured peripheral arterial aneurysm. J Vasc Surg. 2001;34:1127-9.

Kutlu R, Gulcan O, Akbulut A, Turkoz R, Baysal T. Endovascular treatment of huge saccular abdominal aortic aneurysm in a young Behcet patient: mid-term result. BMC Med Imaging. 2002;2:1.

Kwon KB, Shim WH, Yoon YS. Endovascular therapy combined with immunosuppressive treatment for pseudoaneurysms in patients with Behcet's disease. J Endovasc Ther. 2003;10:75-80.

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