Jornal Vascular Brasileiro
https://jvascbras.org/article/doi/10.1590/1677-5449.200201
Jornal Vascular Brasileiro
Case Report

Tratamento endovascular de aneurisma sacular aórtico associado à doença de Adamantiades-Behçet

Endovascular treatment of aortic saccular aneurysms associated with Adamantiades-Behçet disease

Patrick Bastos Metzger; Kamilla Rosales Costa; Simone Lessa Metzger; Leonardo Cortizo de Almeida

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Resumo

Resumo: A doença de Adamantiades-Behçet é uma desordem multissistêmica que se apresenta classicamente com úlceras orais e genitais e envolvimento ocular, podendo o acometimento vascular ocorrer em até 38% dos casos. O envolvimento aórtico é uma das manifestações mais severas e está associado a altas taxas de mortalidade, ocorrendo em 1,5 a 2,7% dos casos. Relatamos um caso de aneurisma sacular de aorta abdominal em um paciente de 49 anos com doença de Adamantiades-Behçet complicada, tratada por correção endovascular.

Palavras-chave

síndrome de Behçet, aneurisma aórtico, procedimentos endovasculares

Abstract

Adamantiades-Behçet disease is a multisystemic disorder that classically presents with oral and genital ulcers and ocular involvement, with vascular involvement in up to 38% of cases. Aortic involvement is one of the most serious manifestations and is associated with high mortality rates, occurring in 1.5 to 2.7% of cases. We report a case of a saccular abdominal aorta aneurysm in a 49-year-old male patient with complicated Adamantiades-Behçet disease that was treated with endovascular repair

Keywords

Behçet syndrome; aortic aneurysm; endovascular procedures.

References

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Submitted date:
10/17/2020

Accepted date:
04/08/2021

60d4c712a9539501482aca32 jvb Articles

J Vasc Bras

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