Jornal Vascular Brasileiro
https://jvascbras.org/article/doi/10.1590/S1677-54492010000200014
Jornal Vascular Brasileiro
Case Report

Tratamento endovascular de aneurismas da aorta em pacientes com doença de Behçet: relato de dois casos

Endovascular treatment of aortic aneurysms in patients with Behcet's disease: report of two cases

Sergio Quilici Belczak; Ricardo Aun; Luisa Valentim; Igor Rafael Sincos; Luciano Dias Nascimento; Pedro Puech-Leão

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Resumo

A doença de Behçet, uma vasculite sistêmica de causa desconhecida, pode ser causa de doença aneurismática da aorta em alguns portadores dessa patologia. Nós apresentamos nossa experiência com dois casos de aneurismas aórticos em pacientes com doença de Behçet submetidos à terapêutica endovascular, descrevendo seus respectivos seguimentos. A terapêutica atual, a patofisiologia e os critérios diagnósticos vigentes foram revisados. Concluímos que a técnica endovascular é uma excelente opção terapêutica para certos pacientes com doença de Behçet e que esta deve ser acompanhada de tratamento imunossupressivo adequado.

Palavras-chave

Doença de Behçet, aneurisma aórtico, terapia endovascular

Abstract

Behcet's disease, a systemic vasculitis of unknown etiology, may be the cause of aortic aneurysmal diseases in some patients. We report our experience with two Behcet's disease patients who presented with aortic aneurysms and were submitted to endovascular therapy, and describe their respective follow-ups. Current pathophysiology, diagnosis, and treatment approaches were reviewed. Our experience suggests that the endovascular approach, combined with adequate immunosuppressive treatment, is an excellent therapeutic option for some patients with Behcet's disease suffering from aneurysms.

Keywords

Behcet's disease, aortic aneurysm, endovascular treatment

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